Ataxic Cerebral Palsy (Ataxia)

Thu 09 May 2024

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By RJ Nealon I often think back to that quick submission loss and tell myself that it was probably the best thing that happened to me and my journey. It forced me to take a deep hard look at myself and converse with my inner self. What do I want? What impact do I want […]

Fri 03 May 2024

Discover how RJ used Brazilian Jiu-Jitsu to find and harness his personal strengths, and how it became an important part of his relationship with his cerebral palsy.

Ataxia is the least common form of cerebral palsy. Ataxia means ‘without order’ or ‘incoordination’.

Ataxic movements are characterised by clumsiness, imprecision, or instability. Movements are not smooth and may appear disorganised or jerky.

The incoordination seen with ataxia occurs when a person attempts to perform voluntary movements such as walking or picking up objects. Ataxia causes an interruption of muscle control in the arms and legs, resulting in a lack of balance and coordination.

People with ataxia may have:

  • Unsteady, shaky movements or tremor
  • Difficulties maintaining balance
  • People with ataxia appear very unsteady and shaky because their sense of balance and depth perception is affected.

What causes ataxia?

Ataxia results from damage to the cerebellum. The cerebellum is the balance centre of the brain. The cerebellum fine-tunes movement commands in order to compensate for whatever posture is being used. It also accounts for the various forces being generated by different parts of the body.

What does ataxia look like?

Ataxia can affect any part of the body and impact upon the movements required to do many day-to-day activities.

It can affect a person’s legs, arms, hands, fingers, speech, eye movements and even muscles involved in swallowing.

Effect on the upper limbs (arms and hands)

When ataxia affects the arms and hands it may cause a tremor or shakiness due to the over-correction of inaccurate movements – this means that when a person reaches for an object, they overshoot the target.

It also results in difficulty performing tasks requiring precise finger movements such as handwriting or using cutlery, or movements that require regular repetition such as clapping.

Effect on the lower limbs (legs)

When ataxia affects walking, a person is unstable and likely to fall. As a result, the person usually walks with the feet spread further apart than the hips, which is known as a ‘wide-base gait’. This is done to try to compensate for their instability and poor balance.

This way of walking can sometimes give the mistaken impression that the person is under the influence of alcohol or drugs. Because their balance is affected, the person may also fall without reason, or be unable to compensate for variations in the ground surfaces or an accidental mild bump from the side.

Effect on speech and swallowing

Ataxia may have an affect on speech and swallowing. When ataxia affects speech, it is sometimes called ‘scanning’ speech – the person uses a monotone voice with a breathy sound; sometimes there are unusual accelerations or pauses between their syllables.

Effect on the eyes

Ataxia may sometimes cause slow eye movements. When ataxia affects the eyes, if the person attempts to change their eye-gaze quickly, their eyes often miss the target. It is like the eye’s overshoot or underestimate their mark and then have to make ‘catch-up’ movements.